Anesthesia & Clinical Research
Open Access
ISSN: 2155-6148
+44 1223 790975
ISSN: 2155-6148
+44 1223 790975
Panni MK
Tanzania
Case Report
Cesarean Section in an Obstetric Patient with Pena-Shokeir Syndrome Type-1, with Partially Corrected Scoliosis with Spinal Rod Placement and History of Malignant Hyperthermia
Author(s): Manimekalai N, Wasiluk I and Panni MKManimekalai N, Wasiluk I and Panni MK
We report a patient with Pena-Shokeir syndrome with severe scoliosis corrected with spinal rod placement from T1-L5, with a known history of malignant hyperthermia presenting for cesarean section. A 21 year old female, 132 cm tall and 35.5 Kg presenting for a primary C-section at 38 weeks with sudden onset of dyspnea, tachypnea, palpitation, and chest pain. A spiral CT demonstrated no pulmonary embolus or any other pathology and clinical symptoms resolved with oxygen and albuterol therapy. The patient had a history of Pena-Shokeir syndrome which included severe myopathy and extreme lower extremity weakness since birth. The patient had contractures of all her major joints, involving both the upper and lower extremities. Additionally she also had cleft palate and severe congenital scoliosis significantly limiting her mobility. Past surgical history included cleft palate repair in childh.. View More»
DOI:
10.4172/2155-6148.1000315