ISSN: 2165-7092
+44 1478 350008
A Guingane, R Sombie, R Da-Ido and A Bougouma
Yalgado Ouedraogo University Hospital, Burkina Faso
Posters & Accepted Abstracts: Pancreat Disord Ther
Objectives: To report a case of Von Hippel-Lindau (VHL) a rare multisystem disease. The interest of our observation lies in the achievement of pancreatic fashion and clinical expression, rarely described and the need to remember that this condition also exists in sub-Saharan Africa should be sought even in the absence of family history VHL. Our observation: Miss GM, 23, consulted in July 2014 for atypical epigastric intermittent pain, abdominal distension without notion of constipation or stopping materials and gas. The patient had VHL disease diagnosed since 2008. Pancreatic MRI had revealed in April 2008 a slightly increased volume pancreas seat multiple cystic formations infra centimeter, the predominant corporeo-caudal region. The family screening revealed that the father, mother and sister are not carriers of the mutation. De novo mutation has been mentioned in the patient. A biology by one against noted high lipase greater than 3N, normoglycemia to 4.66 mmol/ l, CRP at 3 mg/ l, sedimentation rate to 25 mm in the first hour and 47 mm at the second time. Scanner performed remotely symptomatology found an increase in the volume of pancreatic cysts which reached 17 mm without dilation of the pancreatic duct. Conclusion: During a long time visceral lesions of the disease have been underestimated. They are now in the foreground.
A Guingane is a Doctor in Hepato-gastroenterology and has obtained her Master’s in Public Health in 2015. She works at the University Hospital Yalgado Ouedraogo of Ouagadougou in Burkina Faso.
Email: aliceguingane@yahoo.fr