Journal of Clinical & Experimental Dermatology Research
Open Access
ISSN: 2155-9554
ISSN: 2155-9554
Ibtihal Malawi
Umm ALQura University, Saudi Arabia
Posters & Accepted Abstracts: J Clin Exp Dermatol Res
Phakomatosis Pigmentovascularis (PPV) is a rare sporadic developmental disorder characterized by co-existence of a cutaneous vascular malformation and pigmentary nevi. There are different classifications of PPV. When systemic involvement is there, a designation ��?b��? is used, whereas if no systemic involvement, a designation ��?a��? is used. Herein, we reported a 12 years old girl presented with a symptomatic persistent progressive skin lesions since birth. Systemic review and past medical history were all unremarkable. Skin examination revealed mixture of diffuse non-scaly, bleachable erythematous patches, greenish patches and hypopigmented patches over her trunk. Ophthalmologist and neurologist consultations did not reveal any abnormalities. Based on the above clinical findings, the patient was diagnosed to have port-wine stains, Mongolian spots and nevus anemicus. Constellation of these clinical findings without presence of extracutaneous manifestations made the diagnosis of PPV type IIa.
Ibtihal Malawi is currently a Medical Intern graduated from Umm Al-Qura University in Saudi Arabia and is interested in dermatology.
Email: ibtihal661@hotmil.com