Journal of Hepatology and Gastrointestinal disorders
Open Access
ISSN: 2475-3181
+44-20-4587-4809
ISSN: 2475-3181
+44-20-4587-4809
Jennifer S Byrns
Duke University Hospital,
DUMC BOX 3089, Durham, NC 27710
United States
Case Report
Liver Transplantation for the Management of Acute Intermittent Porphyria: A Case Report
Author(s): Matthew R Kappus, Bryant B Summers, Jennifer S Byrns, Carl L Berg and Julius M WilderMatthew R Kappus, Bryant B Summers, Jennifer S Byrns, Carl L Berg and Julius M Wilder
We report a single patient with acute intermittent porphyria whose porphyria was successfully treated with orthotopic liver transplantation. She had a very poor quality of life as a result of years of frequent acute porphyria symptoms manifesting as abdominal pain crises. After transplantation, clinical signs of porphyria resolved as expected. This case adds to a growing body of literature which is assisting to formulate the indications for, and the timing of, transplantation for AIP.
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DOI:
10.4172/2475-3181.1000141